5例先天性肾囊肿病的临床病理分析
作者：王进进
单位：中国福利会国际和平妇幼保健院 上海 200030
关键词：肾囊肿病；尸体解剖；病理特征
诊断病理学杂志000213摘 要：目的了解先天性肾囊肿病的病理特征及分类方法。方法收集5例肾囊肿病尸体解剖资料，观察肾囊肿病病理特点。结果本文5例肾囊肿病分类为多囊性肾发育不良，婴儿型多囊肾均是致死性畸形，预后不良。结论对于这些类型的肾囊肿病，宫内早期诊断十分必要。
分类号：R692 文献标识码：A
文章编号：1007-8096(2000)02-0114-02
Congenital Cystic Kidney Diseases：A Clinicopathological Analysis of 5 Cases
Wang Jinjin
(International Peace Maternity and Child Health Institute of China Welfare Society，Shanghai 200030)
Abstract：Objective To describe the histopathological characteristics of congenital cystic kidney disease(CCKD)and its classification. Methods Pathological features of CCKD were analyzed in 5 cases with autopsy. Results Five cases of CCKDs were classified as multiple cystic hypoplasia and autosomal recessive polycystic kidney diseases，which are malformations to cause infant’s death. Conclusion It is necessary to diagnose CCKD early in uterine and to take measures accordingly.
Keywords：Cystic kidney disease Autopsy Pathological features
参考文献：
[1]Woldo.E.Nelson.Texbook of Podialrics 15tl ed，1999.535-536
[2]王海燕主编.肾脏病学.第二版人民卫生出版社，1996.1253-1265
[3]同济医科大学及中山医科大学编著.外科病理学.第一版.湖北科学技术出版社,1999.673～674
[4]黄澄如.泌尿生殖系统的先天畸形.诸福棠主编.实用外科学.第6版.人民卫生出版社,1996.1554-1556
[5]吉村秀一郎.他.Potter症侯群の4例.周产期医学21:1715-1719.1991
[6]中村靖.他.羊水过少をし胎儿异常ガ疑ゎ症例の超音波断层法 にょ 解析-Potter症侯群を中心とに-周产期医学22:273-276.1992
[7]清水禄子.他.Infantile polycystic Kidney の1例周产期医学24:1025-1028.1994
收稿日期：1999-1l-02
修稿日期：2000-02-04, http://www.100md.com
单位：中国福利会国际和平妇幼保健院 上海 200030
关键词：肾囊肿病；尸体解剖；病理特征
诊断病理学杂志000213摘 要：目的了解先天性肾囊肿病的病理特征及分类方法。方法收集5例肾囊肿病尸体解剖资料，观察肾囊肿病病理特点。结果本文5例肾囊肿病分类为多囊性肾发育不良，婴儿型多囊肾均是致死性畸形，预后不良。结论对于这些类型的肾囊肿病，宫内早期诊断十分必要。
分类号：R692 文献标识码：A
文章编号：1007-8096(2000)02-0114-02
Congenital Cystic Kidney Diseases：A Clinicopathological Analysis of 5 Cases
Wang Jinjin
(International Peace Maternity and Child Health Institute of China Welfare Society，Shanghai 200030)
Abstract：Objective To describe the histopathological characteristics of congenital cystic kidney disease(CCKD)and its classification. Methods Pathological features of CCKD were analyzed in 5 cases with autopsy. Results Five cases of CCKDs were classified as multiple cystic hypoplasia and autosomal recessive polycystic kidney diseases，which are malformations to cause infant’s death. Conclusion It is necessary to diagnose CCKD early in uterine and to take measures accordingly.
Keywords：Cystic kidney disease Autopsy Pathological features
参考文献：
[1]Woldo.E.Nelson.Texbook of Podialrics 15tl ed，1999.535-536
[2]王海燕主编.肾脏病学.第二版人民卫生出版社，1996.1253-1265
[3]同济医科大学及中山医科大学编著.外科病理学.第一版.湖北科学技术出版社,1999.673～674
[4]黄澄如.泌尿生殖系统的先天畸形.诸福棠主编.实用外科学.第6版.人民卫生出版社,1996.1554-1556
[5]吉村秀一郎.他.Potter症侯群の4例.周产期医学21:1715-1719.1991
[6]中村靖.他.羊水过少をし胎儿异常ガ疑ゎ症例の超音波断层法 にょ 解析-Potter症侯群を中心とに-周产期医学22:273-276.1992
[7]清水禄子.他.Infantile polycystic Kidney の1例周产期医学24:1025-1028.1994
收稿日期：1999-1l-02
修稿日期：2000-02-04, http://www.100md.com