摘要:目的 总结Moyamoya病的临床及影像学特征。 方法 回顾性分析南阳市1992年2月～2004年10月经DSA或MRA确诊的31例Moyamoya病患者的临床资料及影像学资料。 结果 31例患者平均年龄25.7岁;脑卒中和头痛是本组Moyamoya病患者最常见的临床表现，发生率分别为83.9%(26例)和74.2%(23例);儿童及青少年患者以缺血性脑卒中发病为主，而成年患者以出血性脑卒中发病为主;所有患者均有颈内动脉或其分支狭窄或闭塞和Moy-amoya血管形成，其中有27例患者的CT或MRI表现为双侧病灶。 结论 对于无脑血管病危险因素的年轻TIA或脑卒中患者，尤其有卒中史或反复头痛发作者则要考虑Moyamoya病的可能;MRA是诊断Moyamoya病的较好的无创检查手段。

    关键词:Moyamoya病;诊断;影像学

    Study on clinical manifestations and imaging characteristics of31Moyamoya disease pateints.

    ZHU Xin-Chen，YANG Fang，GUI Qing-Qiao，et al.

    (Department of Cerebrovascular Diseases，Nanshi Hospital，Nanyang473065，Henan，P.R.China)

    Abstract:Objective To study the clinical manifestation and imaging characteristics of Moyamoya disease. Methods Clini-cal data and imaging data of31patients withMoyamoya diease diagnosed by DSA or MRAwere analyzed retrospectively. Results The mean age of the31patients was25.7years old.Stroke episodes and headaches were the main clinical manifestations with the oc-currence rates of83.9%(26/31)and74.2%(23/31).All patients showed stenosis or occlusion of the internal carotid arteries or their branches and extensive abnormal basicranial vascular network called Moyamoya vascular ......